A case of tuberous sclerosis complex that progressed to end-stage renal disease.

BACKGROUND

A 31-year-old woman with tuberous sclerosis complex presented with a 1 week history of subjective fever, chills, rigors, poor appetite and dizziness.

METHODS

Physical examination, urine and blood analysis, CT of the abdomen, chest and brain, and chest X-ray.

METHODS

End-stage renal disease, septic shock and urinary tract infection secondary to huge bilateral angiomyolipomas of the kidney associated with tuberous sclerosis complex.

RESULTS

Antibiotic therapy, vasopressor treatment and bilateral nephrectomy, followed by hemodialysis while awaiting renal transplantation.