Recurrent retroperitoneal hemorrhage in a patient with tuberous sclerosis complex: a case report.

BACKGROUND

Tuberous sclerosis complex (TSC) is an autosomal dominant disorder. It is characterized by seizures, mental retardation and hamartomatous lesions, including facial angiofibroma, subependymal giant cell astrocytoma, cardiac rhabdomyoma and renal angiomyolipoma (AML). AMLs can bleed severely in the retroperitoneal space.

METHODS

Herein, we present the case of a TSC patient presenting with recurrent severe episodes of retroperitoneal hemorrhage from AMLs successfully managed by angio-embolization.

CONCLUSIONS

Transarterial embolization is effective in preventing and controlling hemorrhage in patients with AMLs of the kidney.