Adult wilms' tumor metastatic to the choroid of the eye.
Ключови думи
Резюме
BACKGROUND
Ocular manifestations of Wilms' tumor are rare, particularly in adults. We present the first reported case of a choroidal metastasis resulting from Wilms' tumor.
METHODS
Case report.
METHODS
A 37-year-old white male with an adult-onset biopsy-proven Wilms' tumor with multiorgan metastatic disease.
RESULTS
We report a unique case of uveal metastasis presumed from a Wilms' tumor. The patient's history included a primary Wilms' tumor with known disseminated metastasis, orbital pain, metamorphopsia, and decreased vision. Ophthalmoscopy revealed a unifocal choroidal tumor in the inferotemporal quadrant of the right eye. Ultrasonographic measurements of the tumor were 4.9 mm in apical height and 15 x 13 mm in basal diameter. Unusual ultrasound findings included echodense stromal opacities and retrobulbar edema. Fluorescein angiography revealed double circulation and late intratumoral fluorescence.
CONCLUSIONS
This is the first reported case of a choroidal metastasis by a Wilms' tumor.