[Double Chambered Right Ventricle with Annuloaortic Ectasia; Report of a Case].

A 61-year-old man presented with lower leg edema, left-sided parasternal systolic heart murmur, and electrocardiographic abnormalities. Transthoracic echocardiography revealed myocardial hypertrophy and severe obstruction of the outflow tract of the right ventricle (RV) with a gradient of 134 mmHg. Cardiac catheterization confirmed the presence of double chambered right ventricle, with a pressure gradient of 84 mmHg between RV inlet and outlet. Chest computed tomography showed his aortic root enlarged to 55 mm. Holter electrocardiogram revealed nonsustained ventricular tachycardia originated from RV outlet. He underwent resection of the muscular band via right ventriculotomy, aortic valve sparing reimplantation using a straight graft in 28 mm diameter, and cryoablation of RV outflow tract under cardiopulmonary bypass. His postoperative course was uneventful. Postoperative examination showed removal of the obstruction of RV outflow tract.