Pediatric Endocrinology Reviews 2004-Aug
Multiple pituitary hormone deficiency (MPHD) associated with normal height, absent puberty and obesity.
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We present a 22-year old girl with MPHD and a normal pituitary imaging (MRI) who grew to normal size without GH. She was very obese. At age 19 years replacement therapy with hydrocortisone, L-thyroxine and sex steroids was started. Despite severe growth hormone deficiency according to the provocative tests and decreased IGF I level our patient grew normally. On follow up at age 22 she is 174cm tall.