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AME Case Rep 2020-Apr

Neuroendocrine Pancreatic Tumor Causing Chronic Diarrhea in Young Adult, a Case Report

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Otávio Filho
Carolina Maués
Frank De Macedo
Saullo Monteiro
Elaine Araújo
Juan Rodriguez
Júlia Cauduro
Maitê Filó
João Bergamasco
Rubem Neto

Ključne riječi

Sažetak

Secretory tumors of vasoactive intestinal polypeptides (VIPomas) are rare neuroendocrine pancreatic neoplasms usually associated with secretory diarrhea. Most cases present themselves with diarrhea, weight loss, and hypokalemia. Although VIPoma patients share easily distinguishable symptoms, early diagnosis remains a challenge. Therefore, tumors are usually found in large proportions and with later staging. The presenting case portrays a unique situation where the tumor found was still in a small size, is worth reporting it to the current literature. The diagnosis was made through laboratory evaluation and imaging studies. The primary treatment consists of exeresis surgery, but cytoreductive surgery also can provide several benefits. This way is necessary to pay attention to diagnoses also in the ways of treatment.

Keywords: Vasoactive intestinal polypeptide (VIPoma); case report; diarrhea; pancreatic neuroendocrine tumor.

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