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Archives de Pediatrie 2007-Dec

[Kawasaki disease in a young infant: difficulties for diagnosis and early complications].

Només els usuaris registrats poden traduir articles
Inicieu sessió / registreu-vos
L'enllaç es desa al porta-retalls
M Saint-Faust
P Benoit
F Bourlon
C Bloch
D De Ricaud

Paraules clau

Resum

We report 1 case of Kawasaki disease in young infant, featuring atypical presentation and severe outcome.

METHODS

A 3-month-old patient was admitted with initial cervical lymphadenitis, and lasting fever. He subsequently developed the classical manifestations of Kawasaki disease. Treatment with intravenous gamma globulins was successful only after a second perfusion. The early echocardiography revealed a coronary vasculitis, which progressed rapidly and was followed by complications as right coronary thrombosis, several aneurysms, and some others as exsudative enteropathy, aseptic meningitis and hepatitis.

CONCLUSIONS

Patients less than 6 months with Kawasaki disease are at increased risk of atypical presentation, severe prognosis and are often predicted to be non-responsive to the first administration of IVIG.

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