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International Journal of Paediatric Dentistry 2011-Jan

Oral manifestations as important symptoms for juvenile dermatomyositis early diagnosis: a case report.

Només els usuaris registrats poden traduir articles
Inicieu sessió / registreu-vos
L'enllaç es desa al porta-retalls
Letícia Machado Gonçalves
José Ribamar Sabino Bezerra-Júnior
Manuel Antonio Gordón-Núñez
Silvana Amado Libério
Adriana de Fátima Vasconcelos Pereira
Maria Carmen Fontoura Nogueira da Cruz

Paraules clau

Resum

BACKGROUND

Juvenile dermatomyositis (JDM) is an idiopathic inflammatory myopathy of childhood and adolescence, characterized by symmetrical weakness of proximal muscles and classical cutaneous features. Literature reports rarely describe or focus on oral lesions that are associated with this disease.

METHODS

This case describes a 4-year-old girl in whom the oral lesions were the initial manifestations of JDM. Physical examination revealed characteristic skin manifestations, proximal muscle weakness, extensive calcinosis, necrotic ulceration, complicated erysipelas, and diffuse alopecia. The diagnosis was established based on the clinical, histological, electroneuromyography, and biochemical findings.

CONCLUSIONS

Recognition of gingival telangiectases as an important diagnostic marker of JDM leads us to suggest that identifying oral manifestations, which may be carried out by a paediatric dentist, contributes in establishing an early diagnosis and an immediate treatment of this condition.

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