Acta neuropathologica. Supplementum 1981
Polysaccharide (amylopectin-like) storage myopathy histochemical ultrastructural and biochemical studies.
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Abstract
A case of an adult polysaccharide myopathy is reported in a patient with progressive muscular atrophy and weakness of limb girdles. Histochemistry and electron microscopy showed in some muscle fibers, a storage material composed of amylopectin-like filaments. Biochemical results were normal and no enzyme deficiency was found. This case is compared with three other published cases. Pathological conditions with amylopectin or amylopectin-like storage material are reviewed.