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Open Medicine (Poland) 2015

Pulmonary arterovenous malformation causing hemothorax in a pregnant woman without Osler-Weber-Rendu syndrome.

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Vincenzo Di Crescenzo
Filomena Napolitano
Alessandro Vatrella
Pio Zeppa
Paolo Laperuta

Märksõnad

Abstraktne

Pulmonary arteriovenous malformations (PAVMs), although most commonly congenital, are usually detected later in life.

METHODS

We present a case of a 19-year-old woman with no previous history of AVM or telangiectasia, who presented dyspnea and hypoxia by massive left hemothorax in the 34th week of gestation. After emergent cesarean delivery, a chest computed tomography (CT) with i.v. contrast showed a likely 3 cm area of active contrast in left lower lung. Chest tube placement revealed about 2 liters of blood. The patient was subsequently found to have pulmonary AVM. A successful embolisation of AVM followed by lung atipic resection involving AVM and decortication for lung re-expansion were the treatments provided.

CONCLUSIONS

Women with known pulmonary AVM should be maximally treated prior to becoming pregnant, and the physician should be alert to complications of pulmonary AVM during pregnancy.

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