[Linear scleroderma "en coup de sabre" causing severe neurological and ocular symptoms]

We present a rare case of a 4-year-old girl suffering from a sclerotic lesion on the forehead as well as uveitis and epileptic seizures. The patient was diagnosed with linear scleroderma "en coup de sabre" (LSECDS). Faced with no gold standard for treatment of LSECDS with severe extracutaneous manifestations, the case was intensively discussed within an interdisciplinary team setting and successfully treated.

Keywords: Histology; Localized scleroderma; Morphea; Pediatric dermatology; Systemic steroids.