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Ophthalmology 2002-Nov

Adult wilms' tumor metastatic to the choroid of the eye.

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Paul T Finger
Floyd A Warren
Yana P Gelman
Steven A McCormick

Ključne riječi

Sažetak

BACKGROUND

Ocular manifestations of Wilms' tumor are rare, particularly in adults. We present the first reported case of a choroidal metastasis resulting from Wilms' tumor.

METHODS

Case report.

METHODS

A 37-year-old white male with an adult-onset biopsy-proven Wilms' tumor with multiorgan metastatic disease.

RESULTS

We report a unique case of uveal metastasis presumed from a Wilms' tumor. The patient's history included a primary Wilms' tumor with known disseminated metastasis, orbital pain, metamorphopsia, and decreased vision. Ophthalmoscopy revealed a unifocal choroidal tumor in the inferotemporal quadrant of the right eye. Ultrasonographic measurements of the tumor were 4.9 mm in apical height and 15 x 13 mm in basal diameter. Unusual ultrasound findings included echodense stromal opacities and retrobulbar edema. Fluorescein angiography revealed double circulation and late intratumoral fluorescence.

CONCLUSIONS

This is the first reported case of a choroidal metastasis by a Wilms' tumor.

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