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Revista do Instituto de Medicina Tropical de Sao Paulo 2019-Aug

Acute petrified myocardium associated with meningococcal sepsis in childhood-onset systemic lupus erythematous: a fatal case.

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Ana Santos
Michele Luglio
Artur Delgado
Constance Schuwartz
Heloísa Marques
Clarissa Valões
Maria Dominguez
Werther de Carvalho
Clovis Silva
Amaro Duarte-Neto

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Abstrè

Acute petrified myocardium associated with septic shock, diagnosed by autopsy has rarely been described. A 15-year-old adolescent male was diagnosed with childhood-onset systemic lupus erythematosus. One year later, he was hospitalized with fever, myalgia, headache, arthritis, vomiting, dyspnea and was diagnosed with sepsis secondary to bronchopneumonia and meningitis. Blood culture identified Neisseria meningitidis serogroup Y. Despite antibiotics and intensive therapeutic measures, he died after 29 days of hospitalization. The autopsy revealed necrotic cardiomyocytes with dystrophic calcification and interstitial fibrosis.

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