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glycogen storage disease/obesitas

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The Use of Uncooked Sweet Polvilho to Treat Hepatic Glycogen Storage Diseases

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A randomize and crossover study will be conducted on two consecutive days, comparing the use of classic cornstarch to the use of sweet polvilho in patients with Glycogen Storage Disease type Ia. Ten patients diagnosed with Glycogen Storage Disease type Ia, confirmed by genetic analysis, will be

Prevalence of Hepatomegaly in Children and Adolescents With Type 1 Diabetes Mellitus

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Type 1 diabetes is a disorder of glucose metabolism that results from insulin deficiency secondary to autoimmune destruction of insulin-secreting β-cells. The prevalence of liver disease among diabetics is estimated to be between 17% and 100%(1). Most of these data were obtained from studies of

Low Carbohydrate Diet: The Effects on Non Alcoholic Fatty Liver Disease in Obese Teens With Metabolic Syndrome

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Specific Aims and Hypothesis: The Primary aim is: To compare the impact of dietary weight loss via carbohydrate-restriction and calorie-restriction on hepatic TG content quantified by H-MRS in obese children with biopsy-proven NAFLD and Met-S. Our Secondary aims are: To compare BMI z-score, ALT
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