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Tunisie Medicale 2010-Sep

[Pseudo tumoral gastric amyloidosis: a case report].

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Entrar Inscrever-se
O link é salvo na área de transferência
Haifa Nfoussi
Ines Chelly
Khadija Bellil
Nidhameddine Kchir
Slim Haouet
Moncef Zitouna

Palavras-chave

Resumo

BACKGROUND

Amyloidosis is an abnormal extracellular deposition of insoluble proteins, which is associated with an involvement of the gastrointestinal tract in 50 to 70% of cases. In primary amyloïdosis (light chain amyloïdosis), localized gastric involvement is a rare finding which can mimick malignancy.

OBJECTIVE

To elucidate the clinical, histological and therapeutic features of pseudo tumoral gastric amyloidosis via a rare report along with a review of related literatures.

METHODS

We report the case of a 56-year-old man, admitted with upper digestive outlet obstruction. Linitis plastica with lymph node involvement was suspected by gastroscopy, barium meal and endoscopic ultrasonography but was not confirmed by gastric biopsies. The patient was treated with total gastrectomy with lymph node dissection. Pathological examination demonstrated gastric and lymph nodes amyloidosis and no malignant tumor was found.

CONCLUSIONS

We propose that amyloidosis should be considered in the differential diagnosis of gastric tumors.

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