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Journal of reproductive medicine, The 2007-Jul

Spontaneous uterine artery rupture during pregnancy in a woman with sickle cell disease: a case report.

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Olivia Fiori
Hervé Prugnolles
Emile Darai
Serge Uzan
Nadia Berkane

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Resumo

BACKGROUND

Spontaneous rupture of uterine vessels during pregnancy is rare and usually involves uteroovarian veins. Presenting symptoms include acute-onset abdominal pain and maternal hypovolemic collapse due to hemoperitoneum. An atypical case of subacute uterine artery rupture at 27 weeks of gestation occurred in a woman with sickle cell disease.

METHODS

A 28-year-old, nulliparous woman with sickle cell disease was admitted at 27 weeks of gestation for sharp abdominal pain radiating to the right flank. The first diagnosis included acute renal colic and a sickling vasoocclusive crisis. One week after admission the patient experienced paroxysmal, diffuse abdominal pain associated with acute fetal distress requiring an emergency cesarean section. Laparotomy revealed an 800-mL hemoperitoneum. Active bleeding from a ruptured uterine artery was observed and successfully treated by selective suture.

CONCLUSIONS

Spontaneous rupture of the uterine artery during pregnancy may present as a 2-step process.

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