Urology Case Reports 2020-May
Virilization of a female infant genitalia caused by a maternal androgen-producing adrenocortical tumor: A case report
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A 4-month-old girl presented us with genital ambiguity. The patient had a persistent urogenital sinus, posterior labial fusion with clitoromegaly. MRI reveals ovary-like mass in left inguinal region and right abdominal cavity. Uterus and vagina was also identified. Her mother was diagnosed with a right androgen-producing adrenocortical tumor 14 months after the birth of a virilized infant.
Keywords: Maternal androgen-producing adrenocortical tumor; Urogenital sinus; Virilization of genitalia.