Archives of Pathology and Laboratory Medicine 1978-Jan
Tuberous sclerosis initially seen as hydrops fetalis: report of a case and review of the literature.
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Povzetek
Hydrops fetalis is a manifestation of tuberous sclerosis that previously has not been reported, to our knowledge. The multiple-organ involvement in this disorder is stressed. Support is given to the hypothesis that tuberous sclerosis represents a widespread tissue dysplasia involving all germ layers.