Indian Pediatrics 2014-Oct
Chronic hypoxemia in a child: thinking outside the box.
Watumiaji waliosajiliwa tu ndio wanaweza kutafsiri nakala
Ingia / Ingia
Kiungo kimehifadhiwa kwenye clipboard
Maneno muhimu
Kikemikali
BACKGROUND
Chronic hypoxemia is generally attributed to primary cardiac or pulmonary entities.
METHODS
A 9-year-old boy presenting with cyanosis, clubbing and hypoxemia, without icterus or hepatosplenomegaly. Cardiovascular and respiratory system examinations were normal.
RESULTS
He was diagnosed as type IB Abernethy malformation, a rare cause of hepatopulmonary syndrome.
CONCLUSIONS
Pediatricians should consider hepatopulmonary syndrome in the differential diagnosis of chronic hypoxemia, even in the absence of jaundice or hepatosplenomegaly.