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Indian Pediatrics 2014-Oct

Chronic hypoxemia in a child: thinking outside the box.

Watumiaji waliosajiliwa tu ndio wanaweza kutafsiri nakala
Ingia / Ingia
Kiungo kimehifadhiwa kwenye clipboard
Barath Jagadisan
Sriram Krishnamurthy
Renitha Raghavan
S Deepak Barathi

Maneno muhimu

Kikemikali

BACKGROUND

Chronic hypoxemia is generally attributed to primary cardiac or pulmonary entities.

METHODS

A 9-year-old boy presenting with cyanosis, clubbing and hypoxemia, without icterus or hepatosplenomegaly. Cardiovascular and respiratory system examinations were normal.

RESULTS

He was diagnosed as type IB Abernethy malformation, a rare cause of hepatopulmonary syndrome.

CONCLUSIONS

Pediatricians should consider hepatopulmonary syndrome in the differential diagnosis of chronic hypoxemia, even in the absence of jaundice or hepatosplenomegaly.

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